KHOÂNG LOÃ VAN 3 LAÙ
1- 3% caùc beänh TBS - 1/10000 - 20000 sô sinh
Tam saéc theå 21 - Hoäi chöùng “Maét meøo”
BS. Ñaøo Höõu Trung
2
- Tim moät thaát
- Taâm thaát chính Traùi
- Khoâng noái tieáp NT - phaûi - Situs Solitus
-Phaânloaïi:
I Ia Ib Ic Khoâng coù CV ÑÑM
II IIa IIb IIc CV ÑÑM Type D
III CV ÑÑM Type L
ÑÒNH NGHÓA - ÑÒNH DANH -
PHAÂN LOAÏI
3
Van 3 laù - Khoâng phaùt trieån - Xô hoaù - Maøng
Nhó phaûi - Daøy - 10% juxtaposition atriale
TLN nhieàu tyùp
Thaát traùi - Buoàng thaát chính - Daøy daõn tuøy thuoäc löôïng
maùu leân phoåi
Thaát phaûi - Thaát phuï 2 thaønh phaàn
Thoâng lieân thaát thöôøng laø haïn cheá
Giaûi phaãu beänh lyù
4
3 yeáu toá
- Kích thöôùc loã TLN
- Coù hay khoâng heïp ÑMP + Ch/vò ?
- Kích thöôùc loã thoâng TLT
Thoâng thöôøng coù 2 theå
- Taêng löôïng maùu leân phoåi - Hieám
- Giaûm löôïng maùu leân phoåi - Nhieàu hôn
Sinh lyù beänh hoïc
5
Anatomic classification of
tricuspid atresia. In about 70% of
cases the great arteries are
normally related, and there is a
small ventricular septal defect
(VDS) with associated hypoplasia
of the pulmonary artery (PA).
When the great arteries are
transposed, the VSD is usually
large, and the Pas are large with
increased pulmonary blood flow.
AS, aortic stenosis ; D-TGA,
complete TGA ; L-TGA,
congenitally corrected TGA ; PA,
pulmonary atresia ; PS,
pulmonary stenosis ; Sub AS,
subaortic stenosis ; Sub PS,
subpulmonary stenosis ; TGA,
transposition of the great arteries
; VSD, ventricular septal defect.
(Data from Keith JD, Rowe RD,
Vlad P : Heart Disease in Infancy
and Childhood, 3rd ed. New York,
Macmillan, 1978)
