
a-Fetoprotein positively regulates cytochrome
c
-mediated caspase
activation and apoptosome complex formation
Lidia Semenkova
1,
*, Elena Dudich
1,
*, Igor Dudich
1
, Natalie Tokhtamisheva
1
, Edward Tatulov
2
,
Yury Okruzhnov
3
, Jesus Garcia-Foncillas
3
, Juan-Antonio Palop-Cubillo
4
and Timo Korpela
5
1
Institute of Immunological Engineering, Moscow, Russia;
2
Anticancer Drug Research Center, Moscow, Russia; Departments of
3
Oncology and
4
Organic Chemistry and Pharmacology, University of Navarra, Pamplona, Spain;
5
Joint Finnish-Russian
Biotechnology Laboratory, Turku University, Finland
Previous results have shown that the oncoembryonic marker
a-fetoprotein (AFP) is able to induce apoptosis in tumor
cells through activation of caspase 3, bypassing Fas-
dependent and tumor necrosis factor receptor-dependent
signaling. In this study we further investigate the molecular
interactions involved in the AFP-mediated signaling of
apoptosis. We show that AFP treatment of tumor cells is
accompanied by cytosolic translocation of mitochondrial
cytochrome c. In a cell-free system, AFP mediates process-
ing and activation of caspases 3 and 9 by synergistic
enhancement of the low-dose cytochrome c-mediated sig-
nals. AFP was unable to regulate activity of caspase 3 in cell
extracts depleted of cytochrome cor caspase 9. Using
high-resolution chromatography, we show that AFP posit-
ively regulates cytochrome c/dATP-mediated apoptosome
complex formation, enhances recruitment of caspases and
Apaf-1 into the complex, and stimulates release of the active
caspases 3 and 9 from the apoptosome. By using a direct
protein–protein interaction assay, we show that pure human
AFP almost completely disrupts the association between
processed caspases 3 and 9 and the cellular inhibitor of
apoptosis protein (cIAP-2), demonstrating its release from
the complex. Our data suggest that AFP may regulate cell
death by displacing cIAP-2 from the apoptosome, resulting
in promotion of caspase 3 activation and its release from the
complex.
Keywords: apoptosis; apoptosome; cytochrome c;IAP-2;
a-fetoprotein.
Apoptotic cell death is characterized by biochemical and
morphological changes, which are largely caused by caspase
activity. A class of cysteine proteases, known as caspases,
which are constitutively expressed in cells as inactive
proenzymes, require proteolytic cleavage to be activated.
In general, either receptor-induced or mitochondrion-
induced death signals stimulate activation of specific
adapterproteinsFADD/MORT1orApaf-1byformation
of the high-molecular-mass death-inducing complex or
apoptosome. The adapter proteins recruit initiator caspases
8 and 9 to activate them by autoprocessing. Once activated,
initiator caspases are ready to induce processing of down-
stream effector caspases 3 and 7 [1]. The mitochondrial
apoptosis pathway is mediated by cytochrome c(cyt-c)
release with the subsequent formation of the Apaf-1/cyt-c/
dATP/procaspase 9 apoptosome complex, leading to acti-
vation of caspase 9 and downstream effector caspases [2].
Chromatographic analysis of the apoptosome assembly
indicated that, in native cell lysates, Apaf-1 oligomerizes
into multimeric complexes of molecular mass 1.4 MDa
and 700 kDa, which in addition to processed caspase 9,
contain fully processed caspase 3 and 7 [3]. Caspases are
inhibited by a number of cellular inhibitor of apoptosis
proteins (cIAPs), which bind directly to procaspases 9 and 3
to prevent their cyt-c-mediated processing and activation
[4,5]. During apoptosis, a mitochondrial protein named
Smac/DIABLO [6] that directly binds to IAPs to remove
them from the apoptosome complex [4,7], cancels the
IAP-mediated caspase inhibition. Recently, another IAP-
inhibitory protein Omi/HtrA2 was characterized, which
operates by abrogation of the IAP–caspase interaction [8].
AFP is the major serum protein of embryonic plasma
that is involved in regulation of gene expression, differen-
tiation, proliferation and apoptosis in developing cells
[9–12]. Although, the biological role of this protein is not
yet fully understood, it has been well characterized as a
physiological carrier/transport protein for various ligands,
including fatty acids, drugs, hormones, heavy metals,
delivering them to developing and malignant cells [9,12].
The specific expression and internalization of AFP is
restricted to developing cells, such as embryonic cells,
activated immune cells and tumor cells, which suggests its
important regulatory role in cell growth and differentiation
[9,10,12]. Various researchers have documented the exist-
ence of specific receptor-dependent mechanisms responsible
for the active endocytosis of AFP by malignant cells [13,14].
Microscopic data have demonstrated that fluoresceinated
Correspondence to E. Dudich, Institute of Immunological Engineering,
142380, Lyubuchany, Moscow Region, Chekhov District, Russia.
Tel./Fax: + 7 095 996 15 55, E-mail: dudich@ineos.ac.ru
Abbreviations: AFP, a-fetoprotein; cyt-c, cytochrome c; cIAP, cellular
inhibitor of apoptosis protein; Ac-DEVD-AMC, Ac-Asp-Glu-Val-
Asp-7-amino-4-methylcoumarin; LEHD-AFC, Leu-Glu-His-Asp-
aminotrifluoromethylcoumarin; IETD-AMC, Ile-Glu-Thr-Asp-7-
amino-4-methylcoumarin; CHO, aldehyde.
*Note: These authors contributed equally to this work.
(Received 11 February 2003, revised 28 August 2003,
accepted 16 September 2003)
Eur. J. Biochem. 270, 4388–4399 (2003) FEBS 2003 doi:10.1046/j.1432-1033.2003.03836.x