Collagen vascular diseases

Vascular Ehlers-Danlos syndrome (vEDS) is a rare autosomal dominant hereditary collagen disease caused by a defect or deficiency in the pro-α1 chain of type III procollagen encoded by the COL3A1 gene. Patients with vEDS rarely present with multiple pneumothoraces.

7p vimaine2711 26-03-2021 16 2   Download

To identify the prognostic factors for survival in patients with interstitial pneumonia with autoimmune features (IPAF) who meet the serological domain of the IPAF criteria. We confirmed that radiological NSIP pattern and age are poor prognostic factors for the survival of IPAF patients.

10p vimaine2711 26-03-2021 13 2   Download

part 1 book “on rounds - 1000 internal medicine pearls” has contents: the clinical evaluation, blood, rheumatology- arthritis, autoimmune and collagen vascular diseases, the heart and circulation, hypertension, hypertension, the kidney and disorders of fluid and acid–base balance, endocrinology and metabolism.

134p tieu_vu13 06-08-2018 38 1   Download

part 2 book “pulmonary pathology - an atlas and text” has contents: small airways, alveolar infiltrates, tobacco-related diseases, diffuse interstitial lung diseases, idiopathic interstitial pneumonias, specific infectious agents, transplant-related pathology, lung pathology in collagen vascular diseases,… and other contents.

785p tieu_vu13 06-08-2018 17 1   Download

(BQ) Continued part 1, part 2 of the document Illustrated manual of pediatric dermatology - Diagnosis and management presents the following contents: Photodermatoses and physical injury and abuse, drug eruptions, pigmentary disorders, collagen vascular diseases, vascular and lymphatic diseases, hair disorders, nail disorders, genodermatoses and syndromes,...

223p thangnamvoiva5 14-07-2016 46 1   Download

(bq) part 1 book "treatment for skin color" presents the following contents: acneiform disorders, bullous and pustular disorders, collagen vascular diseases, eczematous disorders, granulomatous disorders, hypersensitivity and allergic disorders, infectious diseases,...

201p thangnamvoiva5 14-07-2016 48 5   Download

Various systemic diseases (systemic vasculitis-systemic lupus erythematosis, Henoch-Sch¨ onlein purpura, hemolytic ure- mic syndrome, sickle cell disease, and malignancy) and syn- dromes (chromosomal aberrations, Rubinstein-Taybi, Cor- nelia de Lange, and many others) may affect the kidney in childhood [1]. Renal involvement should be excluded in any individual with multisystem disease (collagen disease, diabetes mellitus, and storage diseases). Systemic diseases associated with glomerular abnormalities may present with arthritis, rash, hypertension, hematuria, or proteinuria.

18p connhobinh 10-12-2012 45 1   Download

Eosinophilia Eosinophilia is the presence of 500 eosinophils per µL of blood and is common in many settings besides parasite infection. Significant tissue eosinophilia can occur without an elevated blood count. A common cause of eosinophilia is allergic reaction to drugs (iodides, aspirin, sulfonamides, nitrofurantoin, penicillins, and cephalosporins). Allergies such as hay fever, asthma, eczema, serum sickness, allergic vasculitis, and pemphigus are associated with eosinophilia. Eosinophilia also occurs in collagen vascular diseases (e.g.

5p konheokonmummim 03-12-2010 78 4   Download

Disorders of the Mononuclear Phagocyte System Many disorders of neutrophils extend to mononuclear phagocytes. Thus, drugs that suppress neutrophil production in the bone marrow can cause monocytopenia. Transient monocytopenia occurs after stress or glucocorticoid administration. Monocytosis is associated with tuberculosis, brucellosis, subacute bacterial endocarditis, Rocky Mountain spotted fever, malaria, and visceral leishmaniasis (kala azar).

6p konheokonmummim 03-12-2010 65 4   Download

Systemic causes of nonpalpable purpura fall into several categories, and those secondary to clotting disturbances and vascular fragility will be discussed first. The former group includes thrombocytopenia (Chap. 109), abnormal platelet function as is seen in uremia, and clotting factor defects. The initial site of presentation for thrombocytopenia-induced petechiae is the distal lower extremity.

5p konheokonmummim 30-11-2010 75 4   Download